Diagnostic challenges of the rare Kasabach-Merritt syndrome in an infant

The article is devoted to topical issues of the complexity of the diagnosis of a rare pathology – Kazabach-Merritt syndrome in infants. Against the background of progressive bilateral polysegmental pneumonia, the child retained thrombocytopenia and consumptive coagulopathy. Syndrome-by-syndrome treatment was performed in the intensive care units of the perinatal and pediatric centers of the republican hospital. The patient received a large amount of blood replacement therapy, and the pleural and abdominal cavities were repeatedly drained. In this clinical case, there were no external manifestations of the disease in the form of a tumor on the skin. Initially, the formation was not diagnosed on early CT scans. Kaposiform hemangioendothelioma complicated by Kasabach-Merritt syndrome was suspected by the exclusion method, which was confirmed at the Federal Center. Properly prescribed complex chemotherapy led to an improvement in the baby's condition. In clinical practice, there are often situations where the symptoms of the disease can be masked by other conditions, such as infectious processes or other hemorrhagic disorders. This highlights the importance of a multidisciplinary approach in the diagnosis and treatment of this disease.

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