A clinical case of ANCA-associated systemic vasculitis in a nine-yearold Sakha child
https://doi.org/10.25789/YMJ.2022.78.33
Abstract
ANCA-associated vasculitis (AAV) is a group of diseases characterized by chronic immune inflammation of the wall of small vessels, a polymorphic clinical picture with frequent involvement of the lungs and kidneys, and the presence of circulating autoantibodies to the neutrophil cytoplasm (ANCA). The article presents a clinical case of ANCA-associated systemic vasculitis affecting the lungs and kidneys.
About the Authors
O. N. Ivanova
MI, M.K. Ammosov NEFU
Russian Federation
Russian Federation
Ivanova Olga N. – Ph.D. in medical sciences, Professor, Department of Pediatrics and Pediatric Surgery
V. M. Argunova
CRC at the Republican Hospital No.1
Russian Federation
Russian Federation
Argunova Vera M. – Head of the Department
P. A. Sleptsova
Republican Hospital No.1
Russian Federation
Russian Federation
Sleptsova Polina A. – physician of the emergency department
M. V. Afonskaya
Republican Clinic No.1-NCM
Russian Federation
Russian Federation
Afonskaya Marina V. – physician at CRC Marina V. – physician at CRC
S. I. Innokentyeva
Republican Hospital № 1 of the National Center for Mental Health
Russian Federation
Russian Federation
Innokentyeva Sargylana I. – physician of CR
I. S. Ivanova
TA MI M.K. Ammosov NEFU
Russian Federation
Russian Federation
Ivanova Irina S. – 2nd year student
T. A. Argunova
Institute of M.K. Ammosov North-East Federal University
Russian Federation
Russian Federation
Argunova Tamara A. – 6th year student of the Department of Psychology
T. E. Burtseva
M.K. Ammosov NEFU, chief researcher and head of the laboratory of the Yakut Scientific Centre for Complex Medical Problems
Russian Federation
Russian Federation
Burtseva Tatiana E. – Ph.D. in medical sciences, professor, Department of Pediatrics and Pediatric Surgery
O. L. Kolobova
Saint-Petersburg State Pediatric Medical University
Russian Federation
Russian Federation
Kolobova Oksana L. – Ph.D. in medical sciences, associate professor, Department of Hospital Pediatrics
Saint-Petersburg
I. A. Chikova
Saint-Petersburg State Pediatric Medical University
Russian Federation
Russian Federation
Chikova Irina A. – Ph.D. in medical sciences, Associate Professor at the Department of Hospital Pediatrics
Saint-Petersburg
A. V. Santimov
Saint-Petersburg State Pediatric Medical University
Russian Federation
Russian Federation
Santimov Andrey V. – Ph.D. in medical sciences, Associate Professor at the Department of Pediatrics
Saint-Petersburg
M. M. Kostik
Saint-Petersburg State Pediatric Medical University
Russian Federation
Russian Federation
Kostik Mikhail M. – Ph.D. in medical sciences, professor, Department of Hospital Pediatrics
Saint-Petersburg
References
1. Dobronravov V.A., Karunnaya A.V., Kazimirchik A.V. [et al.]. ANCA-associated vasculitis with dominant kidney damage: clinical and morphological presentation and outcomes. Nephrology. 2019; 23(6): 29-44. doi: 10.36485/1561-6274-2019-23-6-29-44
2. Kazachkina E.O., Lyugai A.V., Hommyatov M.R. [et al.]. ANCA-associated vasculitis. Journal "Health and education in the 21st century" Moscow. 2018. No.9. P. 92-95.
3. Clinical recommendations "Kidney damage in ANCA-associated vasculitis (ANCA-associated glomerulonephritis)". Moscow, 2021.
4. National recommendations "Diagnosis and treatment of ANCA-associated glomerulonephritis (kidney damage in ANCA-associated vasculitis). Moscow, 2014.
5. Troshina E.A., Yukina M.Yu., Nuralieva N.F. [et al.]. The role of HLA genes: from autoimmune diseases to COVID-19. Problems of Endocrinology. No. 66(4).- P. 9-15. doi: https://doi.org/10.14341/probl12470
6. Frolova N.F. ANCA-associated rapidly progressive glomerulonephritis. Clinical nephrology.- No.3.-2018. P. 72-87. DOI: https://dx.doi.org/10.18565/nephrology.2018.3.72-87
7. Shostak N.A., Klimenko A.A. Systemic vasculitis: new in classification, diagnosis and treatment. Clinician. - 2015. - No 2. - P. 8-12.
8. ARChiVe Investigators Network within the PedVas Initiative. Comparing Presenting Clinical Features in 48 Children With Microscopic Polyangiitis to 183 Children Who Have Granulomatosis With Polyangiitis (Wegener's): An ARChiVe Cohort Study/ Cabral DA, Canter DL, Muscal E. [et al.]// Arthritis Rheumatol.- 2016.- Oct;68(10):2514-26. doi: 10.1002/art.39729. PMID: 27111558.
9. Geetha D. ANCA-Associated Vasculitis: Core Curriculum 2020/ D. Geetha, JA. Jefferson // Am. J. Kidney Dis.-2019;26;pii: S0272-6386(19)30826-1. doi: 10.1053/j.ajkd.2019.04.031.
10. Outcome of ANCA-associated renal vasculitis: a 5-year retrospective study/ Booth AD, Almond MK, Burns A [et al.]. //Am J Kidney Dis 2003;41(4):776–784. doi: 10.1016/s0272-6386(03)00025-8
11. Pathogenesis of Antineutrophil Cytoplasmic Autoantibody–Associated Small-Vessel Vasculitis / JC Jennette, RJ Falk , P Hu [et al.] //Annu Rev Pathol.- 2013;24(8):139–160. doi: 10.1146/annurev-pathol-011811-132453
12. Scott DGI. Epidemiology and clinical features of systemic vasculitis / D.G.I. Scott, R.A. Watts// Сlinical and experimental nephrology.- 2013; № 17 (5).- Р 607-610. DOI:10.1007/s10157-013-0830-8
Review
For citations:
Ivanova O.N., Argunova V.M., Sleptsova P.A., Afonskaya M.V., Innokentyeva S.I., Ivanova I.S., Argunova T.A., Burtseva T.E., Kolobova O.L., Chikova I.A., Santimov A.V., Kostik M.M. A clinical case of ANCA-associated systemic vasculitis in a nine-yearold Sakha child. Yakut Medical Journal. 2022;(2):126-128. https://doi.org/10.25789/YMJ.2022.78.33
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