A clinical case of ANCA-associated systemic vasculitis in a nine-yearold Sakha child
https://doi.org/10.25789/YMJ.2022.78.33
Abstract
ANCA-associated vasculitis (AAV) is a group of diseases characterized by chronic immune inflammation of the wall of small vessels, a polymorphic clinical picture with frequent involvement of the lungs and kidneys, and the presence of circulating autoantibodies to the neutrophil cytoplasm (ANCA). The article presents a clinical case of ANCA-associated systemic vasculitis affecting the lungs and kidneys.
About the Authors
O. N. IvanovaRussian Federation
Ivanova Olga N. – Ph.D. in medical sciences, Professor, Department of Pediatrics and Pediatric Surgery
V. M. Argunova
Russian Federation
Argunova Vera M. – Head of the Department
P. A. Sleptsova
Russian Federation
Sleptsova Polina A. – physician of the emergency department
M. V. Afonskaya
Russian Federation
Afonskaya Marina V. – physician at CRC Marina V. – physician at CRC
S. I. Innokentyeva
Russian Federation
Innokentyeva Sargylana I. – physician of CR
I. S. Ivanova
Russian Federation
Ivanova Irina S. – 2nd year student
T. A. Argunova
Russian Federation
Argunova Tamara A. – 6th year student of the Department of Psychology
T. E. Burtseva
Russian Federation
Burtseva Tatiana E. – Ph.D. in medical sciences, professor, Department of Pediatrics and Pediatric Surgery
O. L. Kolobova
Russian Federation
Kolobova Oksana L. – Ph.D. in medical sciences, associate professor, Department of Hospital Pediatrics
Saint-Petersburg
I. A. Chikova
Russian Federation
Chikova Irina A. – Ph.D. in medical sciences, Associate Professor at the Department of Hospital Pediatrics
Saint-Petersburg
A. V. Santimov
Russian Federation
Santimov Andrey V. – Ph.D. in medical sciences, Associate Professor at the Department of Pediatrics
Saint-Petersburg
M. M. Kostik
Russian Federation
Kostik Mikhail M. – Ph.D. in medical sciences, professor, Department of Hospital Pediatrics
Saint-Petersburg
References
1. Dobronravov V.A., Karunnaya A.V., Kazimirchik A.V. [et al.]. ANCA-associated vasculitis with dominant kidney damage: clinical and morphological presentation and outcomes. Nephrology. 2019; 23(6): 29-44. doi: 10.36485/1561-6274-2019-23-6-29-44
2. Kazachkina E.O., Lyugai A.V., Hommyatov M.R. [et al.]. ANCA-associated vasculitis. Journal "Health and education in the 21st century" Moscow. 2018. No.9. P. 92-95.
3. Clinical recommendations "Kidney damage in ANCA-associated vasculitis (ANCA-associated glomerulonephritis)". Moscow, 2021.
4. National recommendations "Diagnosis and treatment of ANCA-associated glomerulonephritis (kidney damage in ANCA-associated vasculitis). Moscow, 2014.
5. Troshina E.A., Yukina M.Yu., Nuralieva N.F. [et al.]. The role of HLA genes: from autoimmune diseases to COVID-19. Problems of Endocrinology. No. 66(4).- P. 9-15. doi: https://doi.org/10.14341/probl12470
6. Frolova N.F. ANCA-associated rapidly progressive glomerulonephritis. Clinical nephrology.- No.3.-2018. P. 72-87. DOI: https://dx.doi.org/10.18565/nephrology.2018.3.72-87
7. Shostak N.A., Klimenko A.A. Systemic vasculitis: new in classification, diagnosis and treatment. Clinician. - 2015. - No 2. - P. 8-12.
8. ARChiVe Investigators Network within the PedVas Initiative. Comparing Presenting Clinical Features in 48 Children With Microscopic Polyangiitis to 183 Children Who Have Granulomatosis With Polyangiitis (Wegener's): An ARChiVe Cohort Study/ Cabral DA, Canter DL, Muscal E. [et al.]// Arthritis Rheumatol.- 2016.- Oct;68(10):2514-26. doi: 10.1002/art.39729. PMID: 27111558.
9. Geetha D. ANCA-Associated Vasculitis: Core Curriculum 2020/ D. Geetha, JA. Jefferson // Am. J. Kidney Dis.-2019;26;pii: S0272-6386(19)30826-1. doi: 10.1053/j.ajkd.2019.04.031.
10. Outcome of ANCA-associated renal vasculitis: a 5-year retrospective study/ Booth AD, Almond MK, Burns A [et al.]. //Am J Kidney Dis 2003;41(4):776–784. doi: 10.1016/s0272-6386(03)00025-8
11. Pathogenesis of Antineutrophil Cytoplasmic Autoantibody–Associated Small-Vessel Vasculitis / JC Jennette, RJ Falk , P Hu [et al.] //Annu Rev Pathol.- 2013;24(8):139–160. doi: 10.1146/annurev-pathol-011811-132453
12. Scott DGI. Epidemiology and clinical features of systemic vasculitis / D.G.I. Scott, R.A. Watts// Сlinical and experimental nephrology.- 2013; № 17 (5).- Р 607-610. DOI:10.1007/s10157-013-0830-8
Review
For citations:
Ivanova O.N., Argunova V.M., Sleptsova P.A., Afonskaya M.V., Innokentyeva S.I., Ivanova I.S., Argunova T.A., Burtseva T.E., Kolobova O.L., Chikova I.A., Santimov A.V., Kostik M.M. A clinical case of ANCA-associated systemic vasculitis in a nine-yearold Sakha child. Yakut Medical Journal. 2022;(2):126-128. https://doi.org/10.25789/YMJ.2022.78.33