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<article article-type="research-article" dtd-version="1.3" xmlns:mml="http://www.w3.org/1998/Math/MathML" xmlns:xlink="http://www.w3.org/1999/xlink" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xml:lang="ru"><front><journal-meta><journal-id journal-id-type="publisher-id">ymj</journal-id><journal-title-group><journal-title xml:lang="ru">Якутский медицинский журнал</journal-title><trans-title-group xml:lang="en"><trans-title>Yakut Medical Journal</trans-title></trans-title-group></journal-title-group><issn pub-type="ppub">1813-1905</issn><issn pub-type="epub">2312-1017</issn><publisher><publisher-name>ЯНЦ КМП</publisher-name></publisher></journal-meta><article-meta><article-id pub-id-type="doi">10.25789/YMJ.2021.76.19</article-id><article-id custom-type="elpub" pub-id-type="custom">ymj-603</article-id><article-categories><subj-group subj-group-type="heading"><subject>Research Article</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="ru"><subject>АКТУАЛЬНАЯ ТЕМА</subject></subj-group><subj-group subj-group-type="section-heading" xml:lang="en"><subject>ACTUAL TOPIC</subject></subj-group></article-categories><title-group><article-title>Сравнительный анализ длительности спорадических форм болезни двигательного мотонейрона в РС (Я)</article-title><trans-title-group xml:lang="en"><trans-title>Comparative analysis of the duration of sporadic forms of motor neuron disease in the Republic of Sakha (Yakutia)</trans-title></trans-title-group></title-group><contrib-group><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Давыдова</surname><given-names>Т. К.</given-names></name><name name-style="western" xml:lang="en"><surname>Davydova</surname><given-names>T. K.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Давыдова Татьяна Кимовна – к.м.н., в.н.с., руковод. Центра нейродегенеративных заболеваний</p></bio><bio xml:lang="en"><p>Davydova Tatiana Kimovna – Candidate of Medical Sciences, associate researcher, Director of the Center for Neurodegenerative Diseases, Head of the lab.</p></bio><email xlink:type="simple">tanya.davydova.56@inbox.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Шадрина</surname><given-names>С. С.</given-names></name><name name-style="western" xml:lang="en"><surname>Shadrina</surname><given-names>S. S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Шадрина Светлана Семеновна – с.н.с. науч.-иссл. лаб.</p></bio><bio xml:lang="en"><p>Shadrina Svetlana Semyonovna – associate researcher, scientific-research lab.</p></bio><email xlink:type="simple">svetlana.maksimo@mail.ru</email><xref ref-type="aff" rid="aff-2"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Варламова</surname><given-names>М. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Varlamova</surname><given-names>M. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Варламова Марина Алексеевна – н.с.</p></bio><bio xml:lang="en"><p>Varlamova Marina Alekseevna – research associate</p></bio><email xlink:type="simple">varlamova.m@yandex.ru</email><xref ref-type="aff" rid="aff-1"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Шнайдер</surname><given-names>Н. А.</given-names></name><name name-style="western" xml:lang="en"><surname>Schneider</surname><given-names>N. A.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Шнайдер Наталья Алексеевна – д.м.н., проф., в.н.с. Центра персонализированной психиатрии и неврологии; проф., в.н.с.</p><p>г. Санкт-Петербург; г. Красноярск</p></bio><bio xml:lang="en"><p>Schneider Natalia Alekseevna – MD, Prof., associate researcher of the Center for Personalized Psychiatry and Neurology; associate researcher</p><p>St. Petersburg; Krasnoyarsk</p></bio><email xlink:type="simple">NASchnaider@yandex.ru</email><xref ref-type="aff" rid="aff-3"/></contrib><contrib contrib-type="author" corresp="yes"><name-alternatives><name name-style="eastern" xml:lang="ru"><surname>Гончарова</surname><given-names>П. С.</given-names></name><name name-style="western" xml:lang="en"><surname>Goncharova</surname><given-names>P. S.</given-names></name></name-alternatives><bio xml:lang="ru"><p>Гончарова Полина Сергеевна – клинический ординатор Центра персонализированной психиатрии и неврологии</p><p>г. Санкт-Петербург</p></bio><bio xml:lang="en"><p>Goncharova Polina Sergeevna –neurologist-resident of the Center for Personalized Psychiatry and Neurology</p></bio><email xlink:type="simple">po.gon4arova@yandex.ru</email><xref ref-type="aff" rid="aff-4"/></contrib></contrib-group><aff-alternatives id="aff-1"><aff xml:lang="ru"><institution>ЯНЦ КМП</institution><country>Россия</country></aff><aff xml:lang="en"><institution>YSC CMP</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-2"><aff xml:lang="ru"><institution>СВФУ им. М.К. Аммосова</institution><country>Россия</country></aff><aff xml:lang="en"><institution>NEFU named after M.K. Ammosov</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-3"><aff xml:lang="ru"><institution>ФГБУ «Национальный медицинский исследовательский центр психиатрии и неврологии им. В.М. Бехтерева» Минздрава России; ФГБОУ ВО Красноярский государственный медицинский университет им. профессора В.Ф. Войно-Ясенецкого</institution><country>Россия</country></aff><aff xml:lang="en"><institution>Federal State Budgetary Institution "V.M. Bekhterev National Medical Research Center of Psychiatry and Neurology" of the Ministry of Health of Russia; Krasnoyarsk State Medical University named after V.F. Voino-Yasenetsky</institution><country>Russian Federation</country></aff></aff-alternatives><aff-alternatives id="aff-4"><aff xml:lang="ru"><institution>ФГБУ «Национальный медицинский исследовательский центр психиатрии и неврологии им. В.М. Бехтерева» Минздрава России</institution><country>Россия</country></aff><aff xml:lang="en"><institution>FSBI "National Medical Center"</institution><country>Russian Federation</country></aff></aff-alternatives><pub-date pub-type="collection"><year>2021</year></pub-date><pub-date pub-type="epub"><day>04</day><month>05</month><year>2025</year></pub-date><volume>0</volume><issue>4</issue><fpage>81</fpage><lpage>86</lpage><permissions><copyright-statement>Copyright &amp;#x00A9; Давыдова Т.К., Шадрина С.С., Варламова М.А., Шнайдер Н.А., Гончарова П.С., 2025</copyright-statement><copyright-year>2025</copyright-year><copyright-holder xml:lang="ru">Давыдова Т.К., Шадрина С.С., Варламова М.А., Шнайдер Н.А., Гончарова П.С.</copyright-holder><copyright-holder xml:lang="en">Davydova T.K., Shadrina S.S., Varlamova M.A., Schneider N.A., Goncharova P.S.</copyright-holder><license xml:lang="ru" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>Данная работа распространяется под лицензией Creative Commons Attribution 4.0.</license-p></license><license xml:lang="en" license-type="creative-commons-attribution" xlink:href="https://creativecommons.org/licenses/by/4.0/" xlink:type="simple"><license-p>This work is licensed under a Creative Commons Attribution 4.0 License.</license-p></license></permissions><self-uri xlink:href="https://ymj.elpub.ru/jour/article/view/603">https://ymj.elpub.ru/jour/article/view/603</self-uri><abstract><p>В статье описано исследование длительности заболевания у пациентов с разной формой болезни двигательного нейрона (БДН) в РС (Я) в зависимости от этноса, возраста и гендерной принадлежности. Полученные результаты коррелируют с данными исследователей в мире и зависят от комбинированного или изолированного поражения мотонейрона.</p></abstract><trans-abstract xml:lang="en"><p>The article describes a study of the duration of the disease in patients with different forms of motor neuron disease (MND) in the Republic of Sakha (Yakutia), depending on ethnicity, age and gender. The obtained results correlate with the data of researchers in the world and depend on the combined or isolated lesion of the motor neuron.</p></trans-abstract><kwd-group xml:lang="ru"><kwd>болезни двигательного нейрона</kwd><kwd>боковой амиотрофический склероз</kwd><kwd>прогрессирующая мышечная атрофия</kwd><kwd>первичный боковой склероз</kwd></kwd-group><kwd-group xml:lang="en"><kwd>motor neuron diseases</kwd><kwd>amyotrophic lateral sclerosis</kwd><kwd>progressive muscle atrophy</kwd><kwd>primary lateral sclerosis</kwd></kwd-group></article-meta></front><back><ref-list><title>References</title><ref id="cit1"><label>1</label><citation-alternatives><mixed-citation xml:lang="ru">Давыдова T.K. Сравнительный анализ спорадических случаев и семейной формы прогрессирующей мышечной атрофии за 30-летний период (1986-2016 гг.) в РС(Я) / T.K. Давыдова, T.Я. Николаева, Л.Т. Оконешникова // Якутский медицинский журнал. - 2018. – 4 (64). - С. 110-113. 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