ymjЯкутский медицинский журналYakut Medical Journal1813-19052312-1017ЯНЦ КМП10.25789/YMJ.2018.61.17ymj-1071Research ArticleАРКТИЧЕСКАЯ МЕДИЦИНАARCTIC MEDICINEОценка распространенности и структуры врожденных пороков развития в архангельской области в 2012-2014 гг. по данным регистра родов архангельской областиAssessment of prevalence and structure of congenital malformations in Arkhangelsk region in 2012-2014 according to the Birth Register of Arkhangelsk oblastПостоевВ. А.PostoevV. A.

Постоев Виталий Александрович – PhD, ассистент кафедры, зав. архангельской междунар. школой обществ. здоровья

г. Архангельск

PhD, Lecturer, Department of public health, health care and social work, Head of the International School of Public Health

163001, Arkhangelsk, Troickij,51 

vipostoev@yandex.ruМеньшиковаЛ. И.MenshikovaL. I.

Меньшикова Лариса Ивановна – д.м.н., проф., зав. кафедрой

г. Архангельск

Doctor of Science, Professor, Head of the Department of public health, health care and social work

163001, Arkhangelsk, Troickij,51 

menshikova1807@gmail.comУсынинаА. А.UsyninaA. A.

Усынина Анна Александровна – к.м.н., доцент

г. Архангельск

Associated professor, Department of neonatology and perinatology

163001, Arkhangelsk, Troickij,51 

erinat@mail.ruГржибовскийА. М.GrjibovskiA. M.

Гржибовский Андрей Мечиславович – PhD, проф., зав. Центральной науч.-исслед. лаб.

Якутск

PhD, Research Director; professor of the department of public health and heal care, general hygiene and bioethics

163001, Arkhangelsk, Troickij,51 

ОдландЙ.О.OdlandJ.O.

Одланд Йон Ойвинд – PhD, проф. 

г. Тромсё 

PhD, Professor of public health, Department of community medicine 

N-9007, Tromso 

jon.oyvind.odland@uit.noФГБОУ ВО «Северный государственный медицинский университет»РоссияFederal state budgetary educational organization of high education “Northern state medical university”Russian FederationФГБОУ ВО «Северный государственный медицинский университет» ; СВФУ им. М.К. АмосоваРоссияFederal state budgetary educational organization of high education “Northern state medical university” ; Federal state autonomous educational organization of higher education “North-East federal university named after M.K. Ammosov”Russian FederationАрктический ун-т НорвегииНорвегияUiT-The Arctic University of NorwayNorway201826082025015457Copyright © Постоев В.А., Меньшикова Л.И., Усынина А.А., Гржибовский А.М., Одланд Й., 20252025Постоев В.А., Меньшикова Л.И., Усынина А.А., Гржибовский А.М., Одланд Й.Postoev V.A., Menshikova L.I., Usynina A.A., Grjibovski A.M., Odland J.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://ymj.elpub.ru/jour/article/view/1071

Целью исследования стал медико-статистический анализ выявляемости и регистрации врожденных пороков развития (ВПр) в медицинском регистре родов архангельской области.Проведено ретроспективное когортное исследование с использованием данных популяционного регистра родов, включающего сведения о всех исходах беременности в сроке 22 недели и более, особенностях течения беременности, родов и заболеваниях новорожденных за 2012-2014 гг. рассчитана общая распространенность ВПр и нозологических форм ВПр, подлежащих обязательному мониторингу.

Introduction Birth defects (BD) are an important medical and social issue as they represent one of the most important causes of infant mortality and childhood disability. Constant epidemiological surveillance is a core issue in primary prevention of this pathology. The aim of this study was to assess prevalence of birth defects based on population birth registry data. Materials and methods The Arkhangelsk County Birth Registry was used in this retrospective cohort study. Database included information on all births at gestational age 22 and more weeks registered in Arkhangelsk County in 2012-2014. Data on variety of perinatal exposures, pregnancy and delivery complications as well as neonatal diseases were available for detail analysis.Results In 2012-2014, 1870 various birth defects in 1718 newborns were registered in Arkhangelsk County. The total prevalence of BD was 39,9 for 1000 newborns, and the prevalence after exclusion of co-called minor anomalies was 28,6 per 1000 newborns, that significantly higher than the Federal monitoring data for Arkhangelsk region. The most frequent groups of BD were congenital anomalies of circulatory system, congenital malformations and deformations of the musculoskeletal system as well as congenital anomalies of the urinary system. When calculating the prevalence of BD that are subject of mandatory registration in Russia, it was found that their prevalence in the Arkhangelsk County was 6,4 per 1000 newborns in 2012-2014.Conclusion The total prevalence of birth defects, as assessed by the Arkhangelsk County birth registry, was higher than reported by the Federal monitoring. It can be assumed that this population-based tool allows to estimate the total prevalence of congenital anomalies more completely compared to the current Federal monitoring.

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The authors declare that there are no conflicts of interest present.